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Isifo sikashukela
("kishukela insipidus", isifo sikashukela) yisifo esingajwayelekile esenzeka ngenxa yokukhiqizwa okungasebenzi kahle kwe-antidiuretic hormone (vasopressin), noma ukwephulwa kokufakwa kwayo ezinso.
Lesi sifo siholela ekukhulisweni kokuphuma kwamanzi, okuhambisana nokwehla kwezindawo zokuhlinza umchamo nokomelela okuqinile.

Izimbangela nezinhlobo zesifo sikashukela

Izinhlobo ezilandelayo ze-insulin yesifo sikashukela ziyahlukaniswa:

  • I-Renal (Nephrogenic) - kubonakaliswa ukuqoqwa okujwayelekile kwe-vasopressin esegazini, kepha ukumunca kwayo izicubu zezinso kuphazamisekile.
  • Okuphakathi (neurogenic) - kwenzeka ngokuvela okunganele kwe-antidiuretic hormone yi-hypothalamus. Isifo sikashukela i-insipidus yemvelaphi emaphakathi iholela eqinisweni lokuthi i-hormone ikhiqizwa ngamanani amancane. Kuyabandakanyeka ekufakweni kwe-fluid okubuthakathaka kwezicubu zezinso. Ngokuntuleka kwe-vasopressin, inani elikhulu lamanzi likhishwa ezinso.
  • Insipidar - kanye nezingcindezi ezivama njalo kanye namava ezinzwa;
  • IGestagen - kwabesifazane abakhulelwe. Isifo sikashukela i-insipidus ngesikhathi sokukhulelwa sakhiwa ngenxa yokubhujiswa kwe-vasopressin yizakhi ze-enzymatic ze-placenta. Ukomela kanye "nokuphelelwa amandla komchamo" kwenzeka kakhulu ku-trimester yesithathu yokuthinta.
  • I-Idiopathic - ngesizathu esingaziwa, kepha izifundo zemitholampilo zibonisa amathuba aphezulu okudluliselwa kwalesi sifo ngefa.

Izimbangela ezivamile zesifo sikashukela:

I-Neurogenic Nephrogenic Idiopathic
  • Izingqinamba zobuchopho ezithinta i-hypothalamus;
  • Amakhaza edlule (umkhuhlane, i-SARS);
  • Ukuvuvukala kwamalonda (encephalitis);
  • Ukulimala kwethambo;
  • Ukwanda kwengcindezi ye-intracranial;
  • Ukuphazamiseka ekufakweni kwegazi ebuchosheni;
  • Ama-metastases we-Tumor.
  • Ukulimala engxenyeni ye-cortical noma yobuchopho yezinso;
  • I-Sickle cell anemia (isifo esiyifa elivela ngokuvela kwamangqamuzana abomvu egazi);
  • Ukwehluleka kwangempela
  • I-Polycystic (ama-cysts amaningi wezinso zombili);
  • Ukwehla noma ukwanda kokuhlushwa kwe-calcium calcium
  • Ukuthatha umuthi onomphumela onobuthi ezinso (demeclocilin, lithium, amphotericin B).
Ezimweni ezingama-30%, imbangela yalesi sifo iyaqhubeka ingaziwa.

Emuva kokuqukethwe

Izimpawu eziphambili zesifo sikashukela insipidus

Izimbangela zalesi sifo ziningi, kepha izimpawu zesifo ziyafana kuzo zonke izinhlobo zalesi sifo nokuhluka kwazo. Noma kunjalo, ubukhulu besithombe somtholampilo buxhomeke ezimisweni ezi-2 ezibalulekile:

  • Ukuntuleka kwe-antidiuretic hormone;
  • Ukungavikeleki kwe-venal receptor vasopressin.
Ezimweni eziningi, izimpawu zesifo zanda kancane kancane. Esigabeni sokuqala sesiguli, ukoma kuyahlupha, ukuphuma njalo kanye nokuchama ngokweqile. Ngokuthola i-insipidus yesifo sikashukela, kufinyelela kumalitha angama-15 omchamo ngosuku esigulini.
Uma ungaqali ukwelashwa kwalesi sifo ekuqaleni kwesifo, kuzovela ezinye izimpawu:

  • Isifiso sokudla siyancipha, ukuqunjelwa kuvela ngenxa yokwephulwa kokuhlanganiswa kwama-enzymes wokugaya kanye nokuqunjelwa kwesisu;
  • Izicubu ezomile ze-mucous, ukuncipha kwesisindo ngenxa yokulahleka kwamanzi;
  • Isisu esingezansi sanda ngenxa yokuchithwa kwesinye;
  • Ukucabanga kuyancipha;
  • Ukushisa kuyenyuka;
  • Umuntu ukhathala ngokushesha;
  • Ukuqubuka kwe-Urinary kwenzeka.
Ukuphazamiseka kwemizwelo nengqondo kuthuthukisa izimpawu zomtholampilo zalesi sifo.
Ngaphezu kwalokho, nazo ezinye izibonakaliso ze-pathological zalesi sifo ziyavela:

  • Umsebenzi wemizwelo;
  • Ubuhlungu bekhanda nokuqwasha;
  • Kwehliswe ukunakwa nokuhlushwa.

Kunokwehluka kwezimpawu zesifo emadodeni, abesifazane nasezinganeni. Abamele ingxenye yengxenye eqinile yesintu bakhombisa ukwehla komsebenzi wezocansi (libido). Kwabesifazane, izimpawu zesifo zihlanganiswa nokungahambi kahle kokuya esikhathini. Ezimweni eziningi, ngokumelene nesizinda sikashukela i-insipidus, ukukhula kokuzala ukungaboli. Uma lesi sifo savela ngesikhathi sokubeletha kwengane, kungenzeka okukhulu kokuphuphuma kwesisu okuzenzakalelayo.

Emuva kokuqukethwe

Izici zokubonisa kwesifo sikashukela ezinganeni

Izimpawu zesifo sikashukela i-insipidus ezinganeni azihlukile ekubonisweni kwalesi sifo kubantu abadala.
Izimpawu ezithile zesifo enganeni:

  • Ngokuphikisana nesizinda sokungondleki kahle, ingane ithola isisindo esikhulu;
  • Ngemuva kokudla, ukugabha kanye nenausea kuyavela;
  • Ukuhluleka kwe-urinary ebusuku;
  • Ubuhlungu obuhlangene.

Izimpawu ezihlukile zesifo sikashukela ezinsaneni:

  • Ukukhathazeka
  • Ingane “ichama” ngezingxenye ezincane;
  • Ilahlekelwa ngokushesha isisindo;
  • Akanakho ukucwaswa;
  • Ukushisa kuyenyuka;
  • Isigqi senhliziyo siyashesha.

Kuze kube unyaka, ingane ayikwazi ukuveza inhlala-kahle yayo ngamazwi. Uma abazali bengaziboni izimpawu zalesi sifo, uyoba nezimpawu eziholela ekufeni.

Emuva kokuqukethwe

Ukuxilongwa nokwelashwa kwe-insipidus yesifo sikashukela

Ukuxilongwa kwesifo sikashukela i-insipidus kudinga umlando wezinto ezilandelayo:

  • Ingabe kukhona ukungalali ebusuku;
  • Isiguli singakanani sisebenzisa uketshezi ngosuku;
  • Ingabe kunokuxineka kwengqondo noma ukoma okwandayo;
  • Ingabe kunezinkinga zamathumbu kanye ne-endocrine.
Ukuxilongwa okungeziwe kwezinguquko emzimbeni, kufanele uphumelele ukuhlolwa kwelabhoratri futhi uhlolwe emtholampilo nakwezokwazisa:

  • Thola ukungahambi kahle komchamo, ukuhlunga kwezinso;
  • Imisakazo yesikhumba kanye nesihlalo saseTurkey;
  • Yenza i-urology e-excretory yezinso ngokuhlukile;
  • I-Echoencephalography;
  • Yenza i-ultrasound yezinso;
  • Nikeza umchamo ekuhlolweni kweZimnitsky (ukuzimisela kwezindawo zokuhlinza zomchamo).
  • Isiguli sihlolwa yi-neurosurgeon, optometrist kanye ne-neuropathologist.

Emuva kokuqukethwe

Ukwelashwa kwesifo sikashukela insipidus

Ukwelashwa kwesifo sikashukela kususelwa enanini lokulahleka kwamanzi nsuku zonke. Lapho umuntu elahlekelwa ngaphansi kwamalitha ama-4 ngosuku, imithi ayibekiwe, futhi ukulungiswa kwesimo kwenziwa ngokudla.
Ngokulahleka okungaphezu kwamalitha ama-4, ukuqokwa kwama-hormone asebenza njengama-hormone antidiuretic kuyanconywa. Ukukhethwa kokuhlushwa komuthi kwenziwa ngesisekelo sokuthola inani lomchamo lansuku zonke.
Imuphi umuthi obambele i-vasopressin:

  • Desmopressin (Adiuretin);
  • Minirin;
  • I-Miskleron;
  • Carbamazepine;
  • IChlorpropamide.

Ngohlobo lwe-renal lwalesi sifo, kunqunywa i-thiazide diuretics (triampur, hydrochlorothiazide). Ukudambisa ukuvuvukala - indomethacin, ibuprofen.

Ngakho-ke, i-insipidus yesifo sikashukela yisifo esibucayi esinezimpawu ezithile ezinganeni nakubantu abadala. Kudinga ukuxilongwa okugcwele nokwelashwa okufanele.

Emuva kokuqukethwe

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